GAA 抗体 (YA2872)

GAA Antibody (YA2872) is a biotin-conjugated non-conjugated IgG antibody, targeting GAA, with a predicted molecular weight of 105 kDa (observed band size: 120,100,75 kDa). GAA Antibody (YA2872) can be used for WB experiment in human, mouse, rat background.

The related gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to related generate multiple intermediate forms and the mature form of the enzyme. Defects in The related gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants.

2548

Predicted band size: 105 kDa; Observed band size: 120,100,75 kDa

Affinity Purified

Non-conjugated

Unmodified

Signal Transduction

Primary Antibody; Recombinant Rabbit Monoclonal Antibody

Recombinant, Monoclonal

Rabbit

Human, Mouse, Rat

P10253

WB: 1/500-1/1000

WB

液体

Supplied in rabbit IgG in phosphate buffered saline , pH 7.4, 150mM NaCl, 0.02% sodium azide and 50% glycerol.

Stored at -20°C for 1 year. Avoid repeated freeze / thaw cycles.

Shipping with blue ice.

IgG

Endogenous

A synthesized peptide derived from human GAA